Title:Subcutaneous IgG in the Myositis Spectrum Disorders
Volume: 14
Issue: 3
Author(s): Maria Giovanna Danieli*, Chiara Gelardi, Veronica Pedini, Francesco Logullo and Armando Gabrielli
Affiliation:
- Clinica Medica, Dipartimento di Scienze Cliniche e Molecolari, Universita Politecnica delle Marche & Ospedali Riuniti, Ancona,Italy
Keywords:
Cancer-associated myositis, dermatomyositis, myositis spectrum disorders, necrotizing autoimmune myositis, ocular
myositis, overlap myositis, polymyositis, pregnancy, scleromyositis, subcutaneous immunoglobulin.
Abstract: The efficacy of subcutaneous immunoglobulin is reported in several neurological disorders
and, more recently, its use has been extended to other inflammatory diseases, such as the idiopathic
inflammatory myopathies, including polymyositis and dermatomyositis. Due to the rarity of
these disorders, the role of immunoglobulin, administered intravenously or subcutaneously, remains
unclear and poorly investigated. We report our experience about the use of subcutaneous immunoglobulin
in myositis spectrum disorders, from idiopathic inflammatory myopathies to more complex
conditions, such as overlap and cancer-associated myositis or pregnancy.