Title:Pseudocoarctation of the Arch and the Abdominal Aorta: A Review
Volume: 19
Issue: 5
Author(s): Manjappa Mahadevappa*, Prashanth Kulkarni, Lakshay Attri and Nidhi Basavaraj
Affiliation:
- Department of Cardiology, JSS Hospital, JSSAHER, Mysuru, Karnataka 570004, India
Keywords:
Pseudocoarctation, aortic coarctation, aortic aneurysm, aortic dissection, aortic kinking, aortic buckling.
Abstract: Pseudocoarctaion of the aorta is a rare congenital anomaly occurring in isolation or with
other congenital heart diseases. The anatomical basis of the condition is linked to an elongated, redundant
aorta which may affect the arch, or the abdominal aorta rarely giving rise to kink and
buckling without causing any significant functional stenosis. It should be carefully differentiated
from the common true coarctation of the aorta. No clinical features are specific to pseudo coarctation
and are often diagnosed incidentally. Although asymptomatic in the majority, few patients can
have nonspecific symptoms and complications due to aneurysm formation, dissection, or rupture of
the aorta. Hence Pseudocoarctaion should be closely followed for the onset of symptoms or possible
complications. Without recommendations, no specific therapy is indicated in asymptomatic patients,
although symptoms and complications warrant definitive treatment. As the natural history of
the disease is unknown, the condition, when diagnosed, should be closely followed up for the occurrence
of any complications. This article reports a pseudo aortic coarctation involving the arch
and a brief literature review of this rare congenital anomaly.