Title:Rarer Components of a Rare Disease: Accessory Hemidiaphragm and
Horseshoe Lung with Scimitar Syndrome: Two Case Reports
Volume: 20
Author(s): Ozgur I. Koska*Hüdaver Alper
Affiliation:
- Biomedical Imaging Department, Dokuz Eylül University, Kuruçeşme 35390, Buca İzmir, Turkey
Keywords:
Scimitar syndrome, Horseshoe lung, Accessory hemidiaphragm, Pulmonary hypoplasia, Case report, Pulmonary hypoplasia.
Abstract:
Introduction:
Scimitar syndrome is a rare developmental anomaly with an incidence of 2/100.000 births. Major components of this disease are partial anomalous
pulmonary venous drainage, pulmonary hypoplasia, systemic arterialization of the right basal lung, and dextroposition of the heart. Horseshoe lung
and accessory hemidiaphragm are two rarer components of this disease.
Case Presentation:
In this paper, horseshoe lung and accessory diaphragm associated with Scimitar syndrome have been reported in two cases.
Conclusion:
In conclusion, being aware of rare manifestations of rare diseases is important to fully describe the pathologic spectrum of the disease. This will
assist in better management and decision-making process.
